Progress in Pediatric Cardiology
Volume 22, Issue 2 , Pages 179-186 , September 2006

The physiology of the Fontan circulation

  • Andrew Redington

      Affiliations

    • Corresponding Author InformationThe Hospital for Sick Children, 555 University Avenue, Toronto, M5G 1X8, Ontario, Canada. Tel.: +1 416 813 6132; fax: +1 416 813 7547.

References 

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  2. Rosenthal M, Bush A, Deanfield J, Redington A. Comparison of cardiopulmonary adaptation during exercise in children after the atriopulmonary and total cavopulmonary connection Fontan procedures. Circulation. Jan 15 1995;91(2):372–378
  3. Hausdorf G, Schneider M, Konertz W. Surgical preconditioning and completion of total cavopulmonary connection by interventional cardiac catheterisation: a new concept. Heart. 1996;75(4):403–409
  4. Redington AN, Knight B, Oldershaw PJ, Shinebourne EA, Rigby ML. Left ventricular function in double inlet left ventricle before the Fontan operation: comparison with tricuspid atresia. Br Heart J. Oct 1988;60(4):324–331
  5. Gaynor JW, Bridges ND, Cohen MI, et al. Predictors of outcome after the Fontan operation: is hypoplastic left heart syndrome still a risk factor?. J Thorac Cardiovasc Surg. Feb 2002;123(2):237–245
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  9. Penny DJ, Lincoln C, Shore DF, Xiao HB, Rigby ML, Redington AN. The early response of the systemic ventricle during transition to the Fontan circulation: an acute hypertrophic cardiomyopathy?. Cardiol Young. 1992;2:78–84
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  12. Penny DJ, Redington AN. Angiographic demonstration of incoordinate motion of the ventricular wall after the Fontan operation. Br Heart J. Dec 1991;66(6):456–459
  13. Penny DJ, Rigby ML, Redington AN. Abnormal patterns of intraventricular flow and diastolic filling after the Fontan operation: evidence for incoordinate ventricular wall motion. Br Heart J. Nov 1991;66(5):375–378
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  18. Alpert NR, Leavitt BJ, Ittleman FP, Hasenfuss G, Pieske B, Mulieri LA. A mechanistic analysis of the force–frequency relation in non-failing and progressively failing human myocardium. Basic Res Cardiol. 1998;93(Suppl 1):23–32
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  27. Hsia TY, Khambadkone S, Redington AN, Migliavacca F, Deanfield JE, de Leval MR. Effects of respiration and gravity on infradiaphragmatic venous flow in normal and Fontan patients. Circulation. Nov 7 2000;102(19 Suppl 3):III148–III153
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  35. Nakano T, Tominaga R, Nagano I, Okabe H, Yasui H. Pulsatile flow enhances endothelium-derived nitric oxide release in the peripheral vasculature. Am J Physiol Heart Circ Physiol. Apr 2000;278(4):H1098–H1104
  36. Khambadkone S, Li J, de Leval MR, Cullen S, Deanfield JE, Redington AN. Basal pulmonary vascular resistance and nitric oxide responsiveness late after Fontan-type operation. Circulation. Jul 1 2003;107(25):3204–3208

PII: S1058-9813(06)00051-8

doi: 10.1016/j.ppedcard.2006.07.007

Progress in Pediatric Cardiology
Volume 22, Issue 2 , Pages 179-186 , September 2006

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